• Linda G

    Member
    November 19, 2022 at 5:00 pm

    Hi Barry, I am writing from the Uk.  I think you definitely need a Neurologist with experience of MG  and/or an  MG specialist, and maybe get 2 opinions if you can,  and research via google a little so you have an idea of what the immune suppressant drugs do, though they all have similar side affects. Many medical practitioners are  still not fully aware of MG and its idiosyncrasies as it is deemed rare.  I went into MG crisis following swine flu in 2009/10  and  then 10 days in ITU and ventilator and then could not swallow for 18 months. I had been diagnosed with MG  9 months earlier , but I had diagnosed it myself before going to the GP following a google search of my symptoms of some years that had got worse.  The GP seemed unconvinced when I asked for the relevant blood test but it came back positive. Before I caught swine flu I went to the GP  to ask for  sick note for a month  as I had a relapse of swallowing and slurring of speech which was slowly  improving  and was trying  to get a job. He refused.  So I understand your distrust. Later I got a live in job  and explained  the situation to them but within  3 months of starting  the job my symptoms increased then I caught the swine flu.  // The problem with MG  is partly due to its rarity and there is no standard treatment that will always work for everyone.  After swine flu they put me on high dose steroids of 60mg and they said I would see a result in 14 days. I am not sure why they said this as steroids and  many steroid sparing agents take sometimes take 3 months at least to get the full affect with some conditions. This made me think the  steroids were not working after 4 weeks and I asked to lower the dose as I thought they were making me worse.  I discharged myself after 2 months  and moved to  stay with a friend  in London. I  could not eat enough and was in hospital again and was having 60mg Prednisolone daily  this time, and a year later  had my thymus out. Due to the extended period on steroids  (6 months) I finally could eat.   However, everytime the steroids went down to 20mg I would start to relapse. After 3 years I finally agreed to Azathioprine 100 mg daily which again can take  6 months to a year to  work and  steroids were  gradually reduced to 5mg daily.    I then stabilised for some years until I had Renal Nephrotic  Syndrome Minimal change disease and they put the steroids up to 6omg again which rectified the renal problem (water retention at increasingly dangerous levels).  After a year the steroids were down to 5mg again and the renal condition flared up again. So up went the steroids to 6omg. The renal condition is usually only  present in children, and in my research it is advised that if in an adult then to consider  MG or other conditions.  So now,  the Nephrologist is suggesting I change to Tacrolimos as this will control the MG as well as the Renal condition and also stop the skin cancers  which Azathioprine  is renowned for. I have had 2, one on my nose and 1 under my eye. But  I have a friend on the same drug  for years for renal transplant,  and has  had these cancers for years  and they just keep removing them ( and her sister also). I also have  a  very  low white  blood cells count due to the Azathioprine. So understand their reason for changing the medication, but I do not see any mention of Tacrolimus on the Myaware site or generally in the UK, though it was developed in Japan and they seem to use it as the first choice drug MG in Japan. There is  a little research on it but not that much, though deemed  perhaps an increasingly  safe alternative for MG, but as far as I can see it looks like Steroids may still be needed. My neurologist has agreed to the change of medication but neither he nor the nephrologist   can guarantee I will not still have to take steroids  still, or that the Tacrolimos  will  control the  MG. Which means I might go into a crisis again, which I am always fearful I will not recover from properly, as drugs do sometimes stop working  I hear. I still have to make a decision by  April 23 maybe, but I checked with the dermatologist and she says they always default to controlling the primary medical condition, i.e. the myasthenia, and that they can control the cancers, and the rheumatologist said the same about controlling the damage to the bones that steroids do, they give me zolondronic acid IV annually for a couple of years when needed. But all drugs have their side affects and we do not know what will work for those with MG (or anyone really) until we try them. If you have not tried Azathioprine before it is a long standing tried and tested drug but needs 6 to 12 months before it works, 3 months might be ok.  The only reason I have not come off steroids is because the renal condition flares up,but you may not have that problem, it is quite unusual and not necessarily related to MG. You also may not have the skin cancer side affect. But most of these immune suppressant drugs all have similar side affects, which is another reason why I am reluctant to change mine as the new drug may bring the same or worse side affect. I am stable and functioning and very wary of changing, as there are no guarantees and it is I that must suffer, and also to make the decision to an extent. With MG and many conditions, we are always choosing between “the devil and the deep blue sea” there are no easy choices, and as we get older (I am 67) I  feel I cannot expect perfection in my health whereas medical staff may feel obliged by medical  law or  morally to try and  improve the situation, but perhaps there is a point when we patient has to decide  “this far and no further”. I believe 7mg of steroids is what our body produces naturally  but I think there has been recent research that has said that even small dose of steroids i.e 5mg or maybe 12mg  will have its significant  affect over time.  I also have had 2 cataracts due to steroids. It may depend how old you are also as to whether you want to risk staying on 12mg as I think 7mg used be  the aim at one time.  I would ONLY  speak with Neurologist with some experience of MG and/or a MG specialist with regard to your treatment. When I  saw my first consultant he said MG needs to be treated with respect, and it does.  I did not dream in a million years I would end up on a ventilator  3 times and unable to swallow for 18 months.  Now I am very careful  of the medications I take, that I do not go where there is obvious infection risk,  and whether I now do change my staple MG medication that is controlling the MG, and maybe I have been luckier than some, having read comments on this thread. Maybe try and speak with 2 consultants, google the drugs they suggest, and then go with your gut feeling. Maybe you decide to stay with 12mg steroids, but that does still have risks, for diabetes as well. Its always a dilemma. Incidentally, I have also had plasma exchange and IVIg several times with no affect, and mestinon when in my first crisis also with no affect. When in ITU  or in hospital on 3   different occasions they gave me neostigmine  IV which gave immediate relief of severe and dangerous  symptoms for about 2 hours, which on the last visit to ITU they gave me this, and then they  gave me 60mg  mestion (via naso gastric tube) ever 3 hours and this actually avoided my having to me intubated  again.  They were going to give me a higher  mestinon dose every 4 hours but the effect wears  off. So  I had asked for  every  60 mg 3 hours as I had read of a Mother giving her 3 year old this type of dose and I think  it gave  a consistent  low level  assistance  over a 24 hour period.  But the hospital knew me quite well by this time and I had a  very understanding neurologist, and we were all trying to work out how to control the MG.  Which I had made worse as I delayed going onto  the Azathoprine (and the various other options, cellcept etc) as I had never had a severe condition before nor been in hospital as a patient.  I hope this helps and my apologies for it being so long. My MG became very bad because I resisted taking  any drugs and  then stress and life and infection occurred, Swine flu being the major trigger for the first crisis.  I would get it under full  control if you can with one of the immune suppressant drugs, while you are relatively well. But we are each different in our experience of MG and most medical professionals do their best, hopefully you can find one you can trust over time. Immune suppressants or steroid sparing agents such as Azathoprine, cellcept, etc, are designed to get patients of steroids altogether, but  it does not always work as hoped, but it does with some patients. It is all trial and error, as someone has said in this thread, MG sufferers used to die, now we can live a relatively normal life and normal life span, once we are stable with the medications that work for us individually.